Can arise from or involve virtually any structure
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Circumscribed cystic mass with variable density
Typically water density (near 0 HU) or chylous (< -20 HU), and only rarely hemorrhagic
No internal enhancement
Can be multiloculated (± septations) with “feathery” appearance
Soft lesions without mass effect: Easily indented by surrounding structures, such as mesenteric vessels/bowel
Usually hypointense on T1WI MR and hyperintense on T2WI
TOP DIFFERENTIAL DIAGNOSES
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Gastrointestinal duplication cyst
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Peritoneal inclusion cyst
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Cyst or cystic tumor arising from visceral organ
CLINICAL ISSUES
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Symptoms are rare (particularly in adults)
Rare symptoms due to mass effect, superinfection, or internal hemorrhage
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Surgery is treatment of choice when necessary
DIAGNOSTIC CHECKLIST
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Differentiate from other primary cystic lesions or tumors of visceral organs
TERMINOLOGY
Synonyms
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Lymphoepithelial cyst, cystic lymphangioma, mesenteric cyst, lymphatic malformation
Definitions
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Congenital benign malformation of lymphatic system arising due to failure of embryologic lymphatic development
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Generic descriptive term for benign congenital cystic mass arising in mesentery or omentum
IMAGING
General Features
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Best diagnostic clue
Cystic mass (without mass effect) in mesentery or retroperitoneum
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Location
Majority of lymphangiomas arise in head, neck, or axillae
Lymphangiomas of abdomen rare (7% of all lymphangiomas)
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Can involve multiple compartments of peritoneum or retroperitoneum
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Can arise from or involve virtually any structure
Lymphangiomatosis: Widespread lymphangiomas (usually liver, spleen, mediastinum, lungs, mesentery)
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Usually presents in infants and young children
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Size
Few mm to 40 cm in diameter
CT Findings
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Circumscribed cystic mass with variable density
Typically water density (near 0 HU) or chylous (< -20 HU), with lesions rarely demonstrating hemorrhagic contents
Related
Diagnostic Imaging_ Gastrointes - Michael P Federle