Immunoglobulin Light-Chain Amyloidosis (Primary Amyloidosis)

Published on 04/03/2015 by admin

Filed under Hematology, Oncology and Palliative Medicine

Last modified 04/03/2015

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Chapter 39 Immunoglobulin Light-Chain Amyloidosis (Primary Amyloidosis)

Table 39-1 Nomenclature of Amyloidosis

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ABPP, Amyloid β protein precursor; GI, gastrointestinal; SAA, serum amyloid A.

From Gertz MA, Lacy MQ, Dispenzieri A: Immunoglobulin light chain amyloidosis (primary amyloidosis, AL). In Gertz MA, Greipp PR, editors: Hematologic malignancies: Multiple myeloma and related plasma cell disorders. New York, 2004, Springer-Verlag, p 157. Used with permission of Mayo Foundation for Medical Education and Research.

Table 39-2 Syndromes in Primary Amyloidosis

Syndrome Patients (%)
Nephrotic or nephrotic and renal failure 30
Hepatomegaly 24
Congestive heart failure 22
Carpal tunnel 21
Neuropathy 17
Orthostatic hypotension 12

From Gertz MA, Lacy MQ, Dispenzieri A: Amyloidosis. In Mehta J, Singhal S, editors: Myeloma. London, 2002, Martin Dunitz Ltd., p 445. Used with permission.