Extramammary Paget disease is a rare intraepidermal adenocarcinoma that presents on the scrotum in men and vulva in women. It may be misdiagnosed as eczema or tinea.

The disease appears as white to red, scaling or macerated, infiltrated, eroded or ulcerated plaque most frequently observed on the labia majora and scrotum.

Three biopsies were taken before malignant cells were demonstrated at the periphery of this chronic ulcer at the base of the scrotum.