Circuit D

Published on 21/03/2015 by admin

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Last modified 22/04/2025

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Circuit D

STATION 8

This station assesses your ability to communicate appropriate, factually correct information in an effective way within the emotional context of the clinical setting:

STATION 9

This station assesses your ability to take a focused history and explain to the parent your diagnosis or differential management plan:

COMMENTS ON STATION 1

DIAGNOSIS: VENTRICULOSEPTAL DEFECT

With ventriculoseptal defects being the most common congenital cardiac anomaly, these (one would hope) will be the murmurs you are likely to hear. The VSD is a must-know station. You must be able to diagnose this with confidence. For some candidates this will mean hunting high and low for a cardiology clinic or attending a specific course. The advantage of assured diagnosis is not only in the confidence it will give you in the exam but also the examiner will find it much easier to test you. Easy marks are subsequently gained for knowing investigations, antibiotic prophylaxis and indications for surgery. These cannot be asked if you are still deliberating as to whether it is aortic stenosis!

Tips
Exam A loud second heart sound suggests pulmonary hypertension (from a large shunt) until proven otherwise Feel the suprasternal notch (a thrill there means AS, or rarely PS) A thrill means the murmur must be grade 4:

Investigations ECG and CXR (can be done at any hospital so a better first-line investigation) – normal if insignificant/asymptomatic Signs of heart failure:

Diagnosis An asymptomatic murmur suggestive of VSD may be monitored clinically (the confident paediatrician may not even do an ECHO; not wise to suggest in exam if you are not sure!) Management Control congestive cardiac failure (diuretics/captopril)
Maintain normal growth with calorie supplementation
Surgery if pulmonary to systemic flow ratio > 2:1
Good dental hygiene with antibiotic prophylaxis (amoxicillin) for
procedures

REMINDER

All Down’s syndrome children should be routinely sent for an echocardiogram (VSD, AVSD). These children are at high risk of developing pulmonary hypertension and subsequently Eisenmenger’s complex with large shunts.

Heart failure

Neonatal Infancy Any
Hypoplastic left heart VSD SVT
Aortic coarctation AVSD Myocarditis
Aortic stenosis PDA (large) Cardiomyopathy
Tricuspid atresia TAPVD  
Interrupted aortic arch    

COMMENTS ON STATION 2

DIAGNOSIS: HEREDITARY SPHEROCYTOSIS

Contrary to popular belief in the hot, stuffy and brightly lit exam room, it is not always easy to pick up peripheral signs of abdominal disease. When one of the authors mentioned he was unable to detect evidence of anaemia in his patient, her mother immediately said, ‘I know, I have never seen her cheeks look so rosy!’. The examiner admitted the patient looked neither jaundiced nor anaemic despite the diagnosis and the candidate was spared the blushes of admitting he had made up signs he thought should have been there.

Hereditary spherocytosis Tips
Exam Cholecystectomy scar (more likely the older the patient) and a splenectomy scar
Treatment Remember folic acid supplements Pneumococcal, meningococcal and Haemophilus influenzae B immunisation required Lifelong penicillin prophylaxis
Acute management Aplastic crises can occur
Pigmented gallstones present in majority by second decade
Differentials Hereditary elliptocytosis Autoimmune haemolytic anaemia

The mother has had her gallstones removed (also having hereditary spherocytosis!).

COMMENTS ON STATION 3

DIAGNOSIS: CEREBRAL PALSY

There is no excuse for not knowing your neurological exam inside out. The difficulty for some candidates is that, despite knowing how to perform the ‘perfect’ exam, the application and interpretation of the results are still difficult. You are also faced with the problem of guessing what the examiner would like you to do. It is very easy to get distracted from your examination routine because you are concerned about getting the whole answer.

For example, the candidate in our scenario notices the microcephaly and wants to examine the patient’s eyes. The examiner, having demonstrated a spastic gait, is annoyed as he feels he has given a clue to examine the lower limbs. He informs the candidate of this, so they go on to look at the legs. While examining the lower limbs, the examiner then becomes annoyed by the thoroughness of the candidate. Having demonstrated a microcephalic child with a spastic gait he feels you should quickly demonstrate just the increased tone and brisk reflexes. He says, ‘If you’re not quick you won’t have time to look at the eyes’ – which the candidate was stopped from doing in the first place!

It is probably easier to examine peripherally rather than centrally when you are under pressure. Therefore examine the legs first, giving yourself time to collect your thoughts. Don’t be distracted by neurological signs in isolation, i.e. the eye signs must be taken with the microcephaly and spasticity.

As your head doesn’t tend to shrink, it is likely an insult has occurred early in life.

In the neurological exam you must always be thinking:

Learn a good definition of cerebral palsy and know some causes (although in this case you can only give a differential).

Prenatal Genetic
TORCH
IUGR
Maternal alcohol/substance misuse
Perinatal Hypoxic ischaemic encephalopathy
  Ventricular haemorrhage
  Hypoglycaemia
Postnatal Meningitis/encephalitis
Head injury

COMMENTS ON STATION 4

DIAGNOSIS: PREVIOUS PNEUMONIA LEADING TO BRONCHIECTASIS (UNABLE TO DETERMINE THIS FROM INFORMATION GIVEN)

A frustrating element of the exam is sometimes there not being an ‘answer’. Many children are diagnostic dilemmas and have had multiple investigations, many treatments and thousands of membership candidates prodding and poking them. It is easy to convince yourself a sign must be there. To misquote the Jedi Master Yoda: ‘Maybe not. A clinical sign or no clinical sign. There is no maybe.’

Producing a list of possible investigations is of no benefit if you don’t know why you are doing that test.

The differential diagnosis of chronic cough amongst all ages:

History and exam
History and exam
Radio-imaging
Radio-imaging
History/pH study
Exam
Mantoux/CXR
Biopsy/FBC
History and radio-imaging
Immunoglobulins
Sweat test
Protease inhibitor typing

Exam Scars on the chest may be from surgical lines pop(?for antibiotics)
Hyperexpansion:
Without clubbing – asthma or chronic lung disease
With clubbing – cystic fibrosis or bronchiectasis
Other – persistent aspiration, tracheo-oesophageal fistula
Hyperexpansion may be diagnosed clinically (increased AP diameter or displaced liver) or radiologically

It is vital in the respiratory case that an effort is made to assess the presence of clubbing, as you can see from the above table that the differential diagnosis is radically changed.

This child was not clubbed and his chest wall was not overtly hyper- expanded. You are told the cystic fibrosis screen was negative. Further history reveals he had a severe pneumonia a couple of years ago which has left him with permanent lung damage and some evidence of evolving bronchiectasis. Repeated chest infections have been a problem and while you were examining his hands you note a paucity of veins for his age (explaining the need for definitive access).

Causes of clubbing Clubbing is not seen before 6 months of age
Cardiac Congenital cyanotic heart disease Subacute bacterial endocarditis
Respiratory Bronchiectasis/cystic fibrosis
Primary ciliary dyskinesia
Tuberculosis
Empyema
Malignancy
Fibrosis
GI Inflammatory bowel disease Biliary cirrhosis

COMMENTS ON STATION 5

DIAGNOSIS: NEUROFIBROMATOSIS

Unlike Station 4, when the answer might not be obtainable from the examination findings alone, it may be just you who doesn’t have a clue! In this scenario the candidate recognised the large right leg and remembered something about hemihypertrophy and renal masses (suggesting an ultrasound when asked about investigations). He was asked what else he would examine and drew a blank. The examiner then demonstrated the large ipsilateral arm and an even more obvious unilateral tongue enlargement. The candidate had no idea and left deflated and confused, only noticing the café au lait spots as he left the room. Subsequently he passed the station probably just for picking up the original sign. Until you get the mark sheet you do not know how you have performed!

Hemihypertrophy May involve whole side of body or just one limb
May be congenital
Associated with Wilms’ tumours
Occurs in Beckwith-Wiedemann syndrome
Russell-Silver syndrome
Regional overgrowth Neurofibromatosis type 1 (see summary on p.190)
Haemangiomas

COMMENTS ON STATION 6

COMMENTS ON STATION 7

Explanation of a lumbar puncture must be something the candidate has encountered and performed on a number of occasions. There is no best way to do it but it is easy to do it badly and lose easily gained marks. You are being marked on your communication and empathic skills, not your history- taking and management. Therefore don’t get bogged down in whys and wherefores. Asking a mother about the child’s current state of health will instantly lose you marks. If you find it difficult to jump straight into things then make up some background banter; for example:

A generalised answer should include the following:

Ensure the mother understands all you have said.

COMMENTS ON STATION 8

Explaining to a medical student the ethics of withdrawing care is a mammoth task. Healthcare professional interaction is going to become an increasingly prominent part of the communication skills section and should not be off-putting for the candidate. Nine minutes is not really long enough to cover ^ all the salient points, but remember that the instructions implicitly state you need not cover everything. Unless you have interacted with medical students over this issue before it is also difficult to know how to approach this issue. Do you give them a didactic talk or ask them questions on what they know? One author has passed a station using the asking-questions approach, so the College obviously are flexible in their approach.

Ethics will be a vital component to at least one of the communication skills stations. For this scenario, knowledge of the RCPCH guidelines on withdrawing care is essential. There are five situations in which withholding or withdrawing care is acceptable:

How these are discussed or brought up is difficult and, I think, to the candidate’s advantage. Demonstration or awareness of principles will be the important factors. Prowess at teaching, as everyone is aware, is not proportional to the intelligence of the teacher!

A suggested strategy is as follows:

COMMENTS ON STATION 9

An offshoot of the long case but designed to be more representative of clinical practice, the history and management planning station is easy to overlook in revision. Interestingly, because you have two communication skills stations, the station should really only focus on the history taken from parents. As stated in the Introduction, it is difficult not to get tied up in explanation/communication to the parents during your history-taking. It will be important to avoid doing this, especially in this example, as you will have so little time to cover all the necessary ground.

For the station in question the salient points are the ability to differentiate between issues which are important for the GP, i.e. regular medications, stability of condition and emergency treatment, as opposed to those which should be referred to a tertiary centre, such as treatment modalities. Tertiary centre referral is the essence of your management plan but not the answer. What the question is looking for is whether you have enough experience of chronic disease to enable you to start a pathway that provides for the complete needs of the patient:

Nutritional status is vital and easily overlooked, as is the effect of the condition on the family. All these factors are difficult to elucidate in 13 minutes, and in the preparation period it may be worth noting information you need that the GP must be told. There is no harm at the end of the consultation saying, ‘I think we should schedule another appointment to discuss some areas we haven’t covered today’.