Procedure 42 Cleft Hand Reconstruction
Examination/Imaging
Clinical Examination
A cleft hand is considered a longitudinal deficiency affecting the central digits. It is commonly inherited as an autosomal dominant trait with variable penetrance. The condition may be bilateral and may involve the feet. Manske and Halikis have proposed a classification based on the status of the first web space that is useful in planning treatment (Table 42-1).
Patients with a typical cleft hand present with a V-shaped cleft in the center of the hand. This is occasionally associated with absence, polydactyly, and/or syndactyly of one or more digits. The cleft may be minor or major with absence of one or more digits. The absence progresses from the radial to the ulnar side. Polydactyly/syndactyly involves the digits adjacent to the cleft. Proximal muscle tendon units and nerves may be variably absent.
There is a strong genetic component associated with hand clefts, and genetic counseling is helpful.
Type | Description | Characteristics |
---|---|---|
I | Normal web | Thumb web space is not narrow |
IIA | Mildly narrowed web | Thumb web space is mildly narrow |
IIB | Severely narrowed web | Thumb web space is severely narrowed |
III | Syndactylized web | Thumb and index rays syndactylized, web space obliterated |
IV | Merged web | Index ray suppressed, thumb web space merged with the cleft |
V | Absent web | Thumb elements suppressed, ulnar rays remain, thumb web space no longer present |
Imaging
Radiographs of the hand and upper limb are necessary for all congenital hand problems to identify other areas of concern.
Metacarpal anomalies are frequently noticed. These include absence of metacarpals within the cleft, transverse tubular bones that widen the cleft with growth, bifid metacarpals supporting one finger, and duplication. Phalangeal anomalies include longitudinally bracketed epiphyses or double phalanges.