Procedure 37 Duplicated Thumb Reconstruction
See Video 31: Duplicated Thumb Reconstruction
Indications
The goal of thumb reconstruction is to restore an acceptable appearance without compromising existing function. Although a child with thumb duplication can function perfectly without reconstruction, the stigma associated with an uncorrected deformity may be unacceptable for the child or the parents, or both.
Reconstruction should be considered at about 12 months of age, before the development of significant deviation deformity and because of the ease of general anesthesia. Furthermore, dissection of anatomic structures is easier compared with younger ages, and the development of pinch grasp occurs at about 12 months.
Examination/Imaging
Clinical Examination
The classification of duplicated thumb is based on the level of duplication, which ranges from type I, which is partial split of the distal phalanx, to type VII, which is complete split of the metacarpal (Table 37-1). The type corresponds to the number of abnormal skeletal elements present. For example, type III has three abnormal bones (two distal phalanges and a partially split proximal phalanx). Wassel type IV is the most common type (Fig. 37-1).
Genetic counseling is usually not necessary except for type VII, which is associated with other congenital anomalies and is inherited in an autosomal dominant pattern.
The duplicated elements are abnormal in size and shape, and the radial duplicate is typically smaller in size. The surgeon should examine the thumb for the level of duplication, the degree of hypoplasia of each component, stability of the involved joints, and position of the thumb with respect to the bony axis and first web space.
Imaging
Preoperative radiographs are indicated to identify the size and number of duplicated skeletal elements and to determine whether the elements are attached (bifid) or separated (duplicate) (Fig. 37-2).
The osseous anatomy is abnormal, with varying degrees of bony hypoplasia as well as widening and angulation of the articular surfaces.
Surgical Anatomy
The flexor and extensor tendons are split and insert eccentrically. An abnormal connection between the flexor and extensor tendons on the radial aspect of the thumb often exists as well. The origins and insertions of the thenar musculature, particularly the opponens pollicis (OP), are aberrant in cases of proximal duplication. The abductor pollicis brevis (APB) and flexor pollicis brevis (FPB) insert into the proximal phalanx of the radial duplicate, whereas the OP inserts into the radial metacarpal. The net effect of the long flexor tendons is to pull the distal phalanges into convergence while the thenar insertions create divergence at the proximal phalangeal level, creating a zigzag deformity (Fig. 37-3).
The arterial supply of the duplicated thumb most commonly consists of a single digital artery located on the ulnar side of the ulnar and radial duplicates, in 74% of cases. Twelve percent of patients exhibit three digital arteries, located on the radial and ulnar sides of the ulnar duplicate and the ulnar side of the radial duplicate. Ten percent of patients exhibit four digital arteries, and 5% maintain a single digital artery associated with the ulnar duplicate.
Stability of the thumb is maintained by the ulnar collateral ligament, and typically the ulnar thumb is retained to preserve this structure.
Positioning
The procedure is conducted under general anesthesia with the patient placed supine on the operating room table. The entire upper extremity is prepared and draped after a tourniquet is applied.
Intraoperative fluoroscopy is often required, and the operative table is positioned to allow easy access for the C-arm.
Exposures
When removing the radial thumb, one must retain a periosteal flap from the radial collateral ligament of the resected thumb to reconstruct the radial collateral ligament of the retained thumb. The extensor tendon from the resected thumb can be transferred to the ulnar side of the retained thumb for tendon.
We describe the reconstruction of a type III and type IV thumb duplication.